Refractory pulmonary artery aneurysm in Behçet’s disease

Pulmonary artery aneurysm (PAA) is a life-threatening complication of Behçet’s disease (BD). Massive hemoptysis secondary to PAAs requires emergent endovascular treatments or surgeries. No endovascular occlusion for pulmonary artery trunk has been reported and no therapeutic algorithm exists for the rare disease. We present an endovascular occlusion and a salvage pneumonectomy for a refractory right main PAA in BD, and provide a proposal of a therapeutic algorithm.